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=> 2010-03-03 ) [11] => stdClass Object ( [ID] => 883 [post_parent] => 70 [post_title] => Guide to Galactosemia and Primary Ovarian Insufficiency (POI) [post_name] => galactosemia-and-primary-ovarian-insufficiency-poi [date] => 2010-01-05 ) [12] => stdClass Object ( [ID] => 74 [post_parent] => 5 [post_title] => Fatty Acid Oxidation Disorders [post_name] => fatty-acid-oxidation-disorders [date] => 2010-03-02 ) [13] => stdClass Object ( [ID] => 1010 [post_parent] => 883 [post_title] => Just for Parents - Your Guide to Talking to Your Daughter About Galactosemia and POI [post_name] => parents-daughter-galactosemia-poi [date] => 2010-01-06 ) [14] => stdClass Object ( [ID] => 1012 [post_parent] => 883 [post_title] => For Women with Galactosemia and POI - Your Guide to Taking Action [post_name] => guide-for-women-galactosemia-poi [date] => 2010-01-06 ) [15] => stdClass Object ( [ID] => 1014 [post_parent] => 883 [post_title] => Other Resources for Families and Women with Galactosemia and POI [post_name] => resources-galactosemia-poi [date] => 2010-01-06 ) [16] => stdClass Object ( [ID] => 1016 [post_parent] => 883 [post_title] => Words to Know - A POI Glossary [post_name] => poi-glossary [date] => 2010-01-06 ) [17] => stdClass Object ( [ID] => 76 [post_parent] => 5 [post_title] => Organic Acid Disorders [post_name] => organic-acid-disorders [date] => 2010-03-03 ) [18] => stdClass Object ( [ID] => 1221 [post_parent] => 5 [post_title] => Teen Challenge [post_name] => teen-challenge [date] => 2010-03-01 ) [19] => stdClass Object ( [ID] => 1335 [post_parent] => 5 [post_title] => Family Weekends [post_name] => family-weekends [date] => 2010-03-01 ) [20] => stdClass Object ( [ID] => 9 [post_parent] => 0 [post_title] => For Professionals [post_name] => for-professionals [date] => 2010-01-13 ) [21] => stdClass Object ( [ID] => 123 [post_parent] => 9 [post_title] => Acute Illness Protocols [post_name] => acute-illness-protocols [date] => 2009-12-08 ) [22] => stdClass Object ( [ID] => 120 [post_parent] => 9 [post_title] => Newborn Screening Protocols [post_name] => newborn-screening-protocols [date] => 2009-12-11 ) [23] => stdClass Object ( [ID] => 426 [post_parent] => 123 [post_title] => Urea Cycle Disorders [post_name] => urea-cycle-disorders [date] => 2009-12-08 ) [24] => stdClass Object ( [ID] => 132 [post_parent] => 9 [post_title] => Health Care Resources [post_name] => health-care-resources [date] => 2010-03-05 ) [25] => stdClass Object ( [ID] => 305 [post_parent] => 426 [post_title] => Neonate with Hyperammonemia [post_name] => neonate-with-hyperammonemia [date] => 2009-10-20 ) [26] => stdClass Object ( [ID] => 717 [post_parent] => 9 [post_title] => Prenatal Education Resources [post_name] => prenatal-education-resources [date] => 2009-12-05 ) [27] => stdClass Object ( [ID] => 439 [post_parent] => 426 [post_title] => Infant/Child with Hyperammonemia [post_name] => infantchild-with-hyperammonemia [date] => 2009-10-30 ) [28] => stdClass Object ( [ID] => 441 [post_parent] => 426 [post_title] => Ornithine Transcarbamylase Deficiency (OTC) [post_name] => ornithine-transcarbamylase-deficiency-otc [date] => 2009-10-30 ) [29] => stdClass Object ( [ID] => 953 [post_parent] => 9 [post_title] => Psychologists' Resources [post_name] => psychologists-resources [date] => 2009-12-24 ) [30] => stdClass Object ( [ID] => 443 [post_parent] => 426 [post_title] => Carbamyl Phosphate Synthetase Deficiency (CPS) [post_name] => carbamyl-phosphate-synthetase-deficiency-cps [date] => 2009-10-30 ) [31] => stdClass Object ( [ID] => 445 [post_parent] => 426 [post_title] => Argininosuccinic Acid Synthetase Deficiency (Citullinemia) (AS) [post_name] => argininosuccinic-acid-synthetase-deficiency-citullinemia-as [date] => 2009-10-30 ) [32] => stdClass Object ( [ID] => 447 [post_parent] => 426 [post_title] => Argininosuccinic Acid Lyase Deficiency (ASA) [post_name] => argininosuccinic-acid-lyase-deficiency-asa [date] => 2009-10-30 ) [33] => stdClass Object ( [ID] => 812 [post_parent] => 9 [post_title] => Transition to Adult Care [post_name] => transition-to-adult-care [date] => 2009-12-08 ) [34] => stdClass Object ( [ID] => 449 [post_parent] => 426 [post_title] => Arginase Deficiency [post_name] => arginase-deficiency [date] => 2009-10-30 ) [35] => stdClass Object ( [ID] => 430 [post_parent] => 123 [post_title] => Fatty Acid Oxidation Disorders [post_name] => fatty-acid-oxidation-disorders [date] => 2009-12-08 ) [36] => stdClass Object ( [ID] => 451 [post_parent] => 430 [post_title] => Very Long Chain Acyl-CoA Dehydrogenase Deficiency (VLCADD) [post_name] => very-long-chain-acyl-coa-dehydrogenase-deficiency-vlcadd [date] => 2009-11-02 ) [37] => stdClass Object ( [ID] => 453 [post_parent] => 430 [post_title] => Long Chain Hydroxy Acyl-CoA Dehydrogenase Deficiency ( LCHADD) [post_name] => long-chain-hydroxy-acyl-coa-dehydrogenase-deficiency-lchadd [date] => 2009-11-02 ) [38] => stdClass Object ( [ID] => 455 [post_parent] => 430 [post_title] => 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[post_name] => photos [date] => 2010-03-01 ) [68] => stdClass Object ( [ID] => 745 [post_parent] => 717 [post_title] => Newborn Screening Guide for Prenatal Educators [post_name] => newborn-screening-guide-for-prenatal-educators [date] => 2009-12-04 ) [69] => stdClass Object ( [ID] => 726 [post_parent] => 717 [post_title] => Newborn Screening Prenatal Curriculum [post_name] => newborn-screening-prenatal-curriculum [date] => 2009-12-04 ) [70] => stdClass Object ( [ID] => 900 [post_parent] => 897 [post_title] => The History of Newborn Screening [post_name] => the-history-of-newborn-screening [date] => 2009-12-17 ) [71] => stdClass Object ( [ID] => 1178 [post_parent] => 897 [post_title] => Discovery of Phenylketonuria (PKU) by Dr. Asbjørn Følling [post_name] => discovery-of-pku-dr-asbjorn-folling [date] => 2010-01-13 ) [72] => stdClass Object ( [ID] => 1198 [post_parent] => 897 [post_title] => Discovery of the Diet for PKU by Dr. Horst Bickel [post_name] => discovery-of-the-diet-for-pku-by-dr-horst-bickel [date] => 2010-01-13 ) [73] => stdClass Object ( [ID] => 1200 [post_parent] => 897 [post_title] => Introducing the Newborn Screening Test by Dr. Robert Guthrie [post_name] => introducing-the-newborn-screening-test-by-dr-robert-guthrie [date] => 2010-01-13 ) ) AUTOEXPAND Array ( [0] => for-families [1] => for-professionals [2] => long-chain-hydroxy-acyl-coa-dehydrogenase-deficiency-lchadd [3] => fatty-acid-oxidation-disorders [4] => acute-illness-protocols [5] => for-professionals )
For Professionals
For Families

Long Chain Hydroxy Acyl-CoA Dehydrogenase Deficiency ( LCHADD)

This protocol is for the sick infant/child who has been previously diagnosed with Long Chain Hydroxy Acyl-CoA Dehydrogenase Deficiency ( LCHADD). LCHADD is caused by a defect in the intramitochondrial b-oxidation of fatty acids. It can cause severe hypoketotic hypoglycemia, lethargy, liver dysfunction with hepatomegaly, clotting defect, metabolic acidosis, hyperammonemia cardiomyopathy, and sudden death.

Click to view the complete protocol as a PDF

Disclaimer
The care of patients with metabolic disorders is complex and it is essential that a metabolic specialist be contacted as rapidly as possible. This protocol is only a guideline and should not be used for definitive treatment without metabolic consultation. Please read our Terms of Use.