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=> 2010-03-03 ) [11] => stdClass Object ( [ID] => 883 [post_parent] => 70 [post_title] => Guide to Galactosemia and Primary Ovarian Insufficiency (POI) [post_name] => galactosemia-and-primary-ovarian-insufficiency-poi [date] => 2010-01-05 ) [12] => stdClass Object ( [ID] => 74 [post_parent] => 5 [post_title] => Fatty Acid Oxidation Disorders [post_name] => fatty-acid-oxidation-disorders [date] => 2010-03-02 ) [13] => stdClass Object ( [ID] => 1010 [post_parent] => 883 [post_title] => Just for Parents - Your Guide to Talking to Your Daughter About Galactosemia and POI [post_name] => parents-daughter-galactosemia-poi [date] => 2010-01-06 ) [14] => stdClass Object ( [ID] => 1012 [post_parent] => 883 [post_title] => For Women with Galactosemia and POI - Your Guide to Taking Action [post_name] => guide-for-women-galactosemia-poi [date] => 2010-01-06 ) [15] => stdClass Object ( [ID] => 1014 [post_parent] => 883 [post_title] => Other Resources for Families and Women with Galactosemia and POI 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=> 120 [post_parent] => 9 [post_title] => Newborn Screening Protocols [post_name] => newborn-screening-protocols [date] => 2009-12-11 ) [23] => stdClass Object ( [ID] => 426 [post_parent] => 123 [post_title] => Urea Cycle Disorders [post_name] => urea-cycle-disorders [date] => 2009-12-08 ) [24] => stdClass Object ( [ID] => 132 [post_parent] => 9 [post_title] => Health Care Resources [post_name] => health-care-resources [date] => 2010-03-05 ) [25] => stdClass Object ( [ID] => 305 [post_parent] => 426 [post_title] => Neonate with Hyperammonemia [post_name] => neonate-with-hyperammonemia [date] => 2009-10-20 ) [26] => stdClass Object ( [ID] => 717 [post_parent] => 9 [post_title] => Prenatal Education Resources [post_name] => prenatal-education-resources [date] => 2009-12-05 ) [27] => stdClass Object ( [ID] => 439 [post_parent] => 426 [post_title] => Infant/Child with Hyperammonemia [post_name] => infantchild-with-hyperammonemia [date] => 2009-10-30 ) [28] => stdClass Object ( [ID] => 441 [post_parent] => 426 [post_title] => Ornithine Transcarbamylase Deficiency (OTC) [post_name] => ornithine-transcarbamylase-deficiency-otc [date] => 2009-10-30 ) [29] => stdClass Object ( [ID] => 953 [post_parent] => 9 [post_title] => Psychologists' Resources [post_name] => psychologists-resources [date] => 2009-12-24 ) [30] => stdClass Object ( [ID] => 443 [post_parent] => 426 [post_title] => Carbamyl Phosphate Synthetase Deficiency (CPS) [post_name] => carbamyl-phosphate-synthetase-deficiency-cps [date] => 2009-10-30 ) [31] => stdClass Object ( [ID] => 445 [post_parent] => 426 [post_title] => Argininosuccinic Acid Synthetase Deficiency (Citullinemia) (AS) [post_name] => argininosuccinic-acid-synthetase-deficiency-citullinemia-as [date] => 2009-10-30 ) [32] => stdClass Object ( [ID] => 447 [post_parent] => 426 [post_title] => Argininosuccinic Acid Lyase Deficiency (ASA) [post_name] => argininosuccinic-acid-lyase-deficiency-asa [date] => 2009-10-30 ) [33] => stdClass Object ( [ID] => 812 [post_parent] => 9 [post_title] => Transition to Adult Care [post_name] => transition-to-adult-care [date] => 2009-12-08 ) [34] => stdClass Object ( [ID] => 449 [post_parent] => 426 [post_title] => Arginase Deficiency [post_name] => arginase-deficiency [date] => 2009-10-30 ) [35] => stdClass Object ( [ID] => 430 [post_parent] => 123 [post_title] => Fatty Acid Oxidation Disorders [post_name] => fatty-acid-oxidation-disorders [date] => 2009-12-08 ) [36] => stdClass Object ( [ID] => 451 [post_parent] => 430 [post_title] => Very Long Chain Acyl-CoA Dehydrogenase Deficiency (VLCADD) [post_name] => very-long-chain-acyl-coa-dehydrogenase-deficiency-vlcadd [date] => 2009-11-02 ) [37] => stdClass Object ( [ID] => 453 [post_parent] => 430 [post_title] => Long Chain Hydroxy Acyl-CoA Dehydrogenase Deficiency ( LCHADD) [post_name] => long-chain-hydroxy-acyl-coa-dehydrogenase-deficiency-lchadd [date] => 2009-11-02 ) [38] => stdClass Object ( [ID] => 455 [post_parent] => 430 [post_title] => 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[post_name] => photos [date] => 2010-03-01 ) [68] => stdClass Object ( [ID] => 745 [post_parent] => 717 [post_title] => Newborn Screening Guide for Prenatal Educators [post_name] => newborn-screening-guide-for-prenatal-educators [date] => 2009-12-04 ) [69] => stdClass Object ( [ID] => 726 [post_parent] => 717 [post_title] => Newborn Screening Prenatal Curriculum [post_name] => newborn-screening-prenatal-curriculum [date] => 2009-12-04 ) [70] => stdClass Object ( [ID] => 900 [post_parent] => 897 [post_title] => The History of Newborn Screening [post_name] => the-history-of-newborn-screening [date] => 2009-12-17 ) [71] => stdClass Object ( [ID] => 1178 [post_parent] => 897 [post_title] => Discovery of Phenylketonuria (PKU) by Dr. Asbjørn Følling [post_name] => discovery-of-pku-dr-asbjorn-folling [date] => 2010-01-13 ) [72] => stdClass Object ( [ID] => 1198 [post_parent] => 897 [post_title] => Discovery of the Diet for PKU by Dr. Horst Bickel [post_name] => discovery-of-the-diet-for-pku-by-dr-horst-bickel [date] => 2010-01-13 ) [73] => stdClass Object ( [ID] => 1200 [post_parent] => 897 [post_title] => Introducing the Newborn Screening Test by Dr. Robert Guthrie [post_name] => introducing-the-newborn-screening-test-by-dr-robert-guthrie [date] => 2010-01-13 ) ) AUTOEXPAND Array ( [0] => for-families [1] => for-professionals [2] => very-long-chain-acyl-coa-dehydrogenase-deficiency-vlcadd [3] => fatty-acid-oxidation-disorders [4] => acute-illness-protocols [5] => for-professionals )
For Professionals
For Families

Very Long Chain Acyl-CoA Dehydrogenase Deficiency (VLCADD)

This protocol is for the sick infant/child who has been previously diagnosed with Very long Chain Acyl CoA Dehydrogenase Deficency (VLCADD). VLCADD is an autosomal recessive disorder resulting in an intramitochondrial defect in the b-oxidation of fatty acids. It can cause severe hypoketotic hypoglycemia, encephalopathy, lethargy, liver dysfuction with hepatomegaly,cardiomyopathy metabolic acidosis, hyperammonemia and sudden death.

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Disclaimer
The care of patients with metabolic disorders is complex and it is essential that a metabolic specialist be contacted as rapidly as possible. This protocol is only a guideline and should not be used for definitive treatment without metabolic consultation. Please read our Terms of Use.