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[post_parent] => 426 [post_title] => Ornithine Transcarbamylase Deficiency (OTC) [post_name] => ornithine-transcarbamylase-deficiency-otc [date] => 2009-10-30 ) [29] => stdClass Object ( [ID] => 953 [post_parent] => 9 [post_title] => Psychologists' Resources [post_name] => psychologists-resources [date] => 2009-12-24 ) [30] => stdClass Object ( [ID] => 443 [post_parent] => 426 [post_title] => Carbamyl Phosphate Synthetase Deficiency (CPS) [post_name] => carbamyl-phosphate-synthetase-deficiency-cps [date] => 2009-10-30 ) [31] => stdClass Object ( [ID] => 445 [post_parent] => 426 [post_title] => Argininosuccinic Acid Synthetase Deficiency (Citullinemia) (AS) [post_name] => argininosuccinic-acid-synthetase-deficiency-citullinemia-as [date] => 2009-10-30 ) [32] => stdClass Object ( [ID] => 447 [post_parent] => 426 [post_title] => Argininosuccinic Acid Lyase Deficiency (ASA) [post_name] => argininosuccinic-acid-lyase-deficiency-asa [date] => 2009-10-30 ) [33] => stdClass Object ( [ID] => 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For Professionals
For Families

Maple Syrup Urine Disease (MSUD)

This protocol is for the sick infant/child who has been previously diagnosed with Maple Syrup Urine Disease (MSUD). MSUD is an organic acid disorder but is often classified as an amino acid disorder because of increased levels of branched chain amino acids as well as the organic acids. The central emergency features of MSUD are profound metabolic ketoacidosis and brain edema with lethargy progressing to coma.

Click to view the complete protocol as a PDF

Disclaimer
The care of patients with metabolic disorders is complex and it is essential that a metabolic specialist be contacted as rapidly as possible. This protocol is only a guideline and should not be used for definitive treatment without metabolic consultation. Please read our Terms of Use.