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[post_parent] => 426 [post_title] => Ornithine Transcarbamylase Deficiency (OTC) [post_name] => ornithine-transcarbamylase-deficiency-otc [date] => 2009-10-30 ) [29] => stdClass Object ( [ID] => 953 [post_parent] => 9 [post_title] => Psychologists' Resources [post_name] => psychologists-resources [date] => 2009-12-24 ) [30] => stdClass Object ( [ID] => 443 [post_parent] => 426 [post_title] => Carbamyl Phosphate Synthetase Deficiency (CPS) [post_name] => carbamyl-phosphate-synthetase-deficiency-cps [date] => 2009-10-30 ) [31] => stdClass Object ( [ID] => 445 [post_parent] => 426 [post_title] => Argininosuccinic Acid Synthetase Deficiency (Citullinemia) (AS) [post_name] => argininosuccinic-acid-synthetase-deficiency-citullinemia-as [date] => 2009-10-30 ) [32] => stdClass Object ( [ID] => 447 [post_parent] => 426 [post_title] => Argininosuccinic Acid Lyase Deficiency (ASA) [post_name] => argininosuccinic-acid-lyase-deficiency-asa [date] => 2009-10-30 ) [33] => stdClass Object ( [ID] => 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For Professionals
For Families

Ornithine Transcarbamylase Deficiency (OTC)

This protocol is for the sick infant/child who has previously been diagnosed with OTC deficiency. Hyperammonemic crises in children with urea cycle defects (UCDs) are medical emergencies and must be treated as such to avoid death or serious brain injury.

Click to view the complete protocol as a PDF

Disclaimer
The care of patients with metabolic disorders is complex and it is essential that a metabolic specialist be contacted as rapidly as possible. This protocol is only a guideline and should not be used for definitive treatment without metabolic consultation. Please read our Terms of Use.